Progressive pulmonary vein stenosis in down syndrome infant: a rare cause of pulmonary hypertension
Norazah, Z.; Joyce Darshinee, D.S.
Medical Journal of Malaysia 73(2): 119-120
2018
ISSN/ISBN: 0300-5283 PMID: 29703879 Document Number: 697661
Pulmonary veins stenosis in a Down Syndrome infant with normal connection pulmonary vein is rare and precise incidence of this disease is unknown. We report a case of progressive multiple pulmonary vein stenosis in a Down Syndrome infant with congenital heart disease and transient myeloproliferative leukaemia. This case-report aims to improve awareness among physicians and sonographers of this disease and the importance of pulmonary vein assessment in congenital heart disease with unexplained pulmonary hypertension.
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