Pulmonary capillary haemangiomatosis: a rare cause of pulmonary hypertension
Babu, K.Anand.; Supraja, K.; Singh, R.B.
Indian Journal of Chest Diseases and Allied Sciences 56(4): 259-262
2015
ISSN/ISBN: 0377-9343 PMID: 25962202 Document Number: 683384
Pulmonary capillary haemangiomatosis (PCH) is a rare disorder of unknown aetiology, characterised by proliferating capillaries that invade the pulmonary interstitium, alveolar septae and the pulmonary vasculature. It is often mis-diagnosed as primary pulmonary hypertension and pulmonary veno-occlusive disease. Pulmonary capillary haemangiomatosis is a locally aggressive benign vascular neoplasm of the lung. We report the case of a 19-year-old female who was referred to us in the early post-partum period with severe pulmonary artery hypertension, which was diagnosed as PCH by open lung biopsy.