A operative case for atrial septal defect associated with peripheral pulmonary stenosis and pulmonary hypertension
Tamura, H.; Ogawa, K.; Atobe, M.; Matsumoto, M.; Hiratsuka, H.
Nihon Kyobu Geka Gakkai 28(1): 124-130
1980
ISSN/ISBN: 0369-4739 PMID: 7365297 Document Number: 155400
A case of a 9 yr old girl with peripheral pulmonary stenosis (PPS) associated with atrial septal defect [ASD] and pulmonary hypertension was described. She complained of cyanosis and dyspnea on exertion preoperatively. On cardiac catherization and cardioangiography the pulmonary arterial pressure was 100/20 mm Hg, left-right [L-R] shunt ratio was 39% and reverse shunt ratio 14% with stenosis peripheral pulmonary artery to both main pulmonary arteries. Direct closure of ASD was done, but the areas of stenosis were left untouched. The pulmonary arterial pressure decreased 70/15 mm Hg, but showed pulmonary hypertension, 2 yr after operation. Clinically she became asymptomatic. The cardiac defect accompanied with PPS may be operated upon, even though PPS is inoperable surgically. Hemodynamic stress due to L-R shunt flow may give bad influence upon the pulmonary capillary beds. But serial right catheterization will be necessitated to evaluate the progression of pulmonary artery pressure.