Madelung disease : report of a case and review of the literature
Celentano, V.; Esposito, E.; Perrotta, S.; Giglio, M.C.; Tarquini, R.; Luglio, G.; Bucci, L.
Acta Chirurgica Belgica 114(6): 417-420
2014
ISSN/ISBN: 0001-5458 PMID: 26021689 Document Number: 672149
Madelung disease is a rare disorder characterized by the presence of multiple, symmetric, nonencapsulated fatty accumulations diffusely involving the cheeks, the neck, the upper trunk, the shoulder girdle area, and the upper extremities. The cause of this syndrome is unknown, but it has been associated with alcoholism in 60% to 90% of -patients. The long-term lipomatous deposits are often large and cosmetically deforming, and the upper aerodigestive tract and great veins may be compressed. We report the case of a man with MD, involving the cervical and upper dorsal -regions, who underwent surgical treatment at our Department.