A toddler with an itchy, brown rash
Mulder, K.M.; Vermeer, M.H.
Nederlands Tijdschrift Voor Geneeskunde 160: A9630
2016
ISSN/ISBN: 1876-8784 PMID: 26786799 Document Number: 691400
An otherwise healthy 15-month-old boy presented with a pruritic rash that had gradually developed since birth, leaving brown pigmentation. Darier's sign was positive and the diagnosis of juvenile urticaria pigmentosa was made. Juvenile urticaria pigmentosa usually shows spontaneous remission before puberty. Progression to systemic mastocytosis is extremely rare.