A young woman with progressive cerebral atrophy
Shahbazi Fashtali, S.N.N.; Liauw, L.; Kaanders, J.H.A.M.H.
Nederlands Tijdschrift Voor Geneeskunde 156(37): A3451
2012
ISSN/ISBN: 1876-8784 PMID: 22971426 Document Number: 657319
A 21-year-old patient suffering from neurofibromatosis type 1 had received radiotherapy for a chiasm glioma 17 years ago. Fourteen years later, there was progressive deterioration of several neurological functions. MRI scans showed a progressively increasing volume loss of the left hemisphere and stenoses around the circle of Willis with secondary parenchymal effects. Based on conventional cerebral angiography, the diagnosis 'moyamoya syndrome' was made.