Prosthodontic management of patients with amelogenesis imperfecta
Hoods-Moonsammy, V.J.; Mothopi, M.M.; Taruvingira, A.K.; Owen, C.P.; Howes, D.G.
Sadj Journal of the South African Dental Association 67(7): 409-412
2012
ISSN/ISBN: 1029-4864 PMID: 23951803 Document Number: 656918
Amelogenesis Imperfecta (AI) is an heterogenous genetic disorder that disturbs the developing enamel structure. This rare ectodermal defect leads to a variety of clinical manifestations due to agenesis, hypoplasia, and/or hypomineralisation of the enamel. To describe the prosthodontic management of dental anomalies commonly associated with AI. By using the classification of Witkop and Rao (1971), the variation in clinical presentation of the different Types of AI are illustrated and discussed, in particular Type I AI and Type 4 AI. Early diagnosis and prosthodontic management as part of a multidisciplinary, patient-centred approach are key factors to treatment success. Treatment options to address the oral complications are influenced by modifying factors including age, socioeconomic status, type and severity of the disorder, and intraoral status at the time of treatment planning. Ultimately, management includes pain and infection control, provision of aesthetics and restoration of function which may lead to patient satisfaction, psychological well-being and an improved quality of life.