Papillon-Lefevre syndrome: two case reports
Shah, J.; Goel, S.
Indian Journal of Dental Research Official Publication of Indian Society for Dental Research 18(4): 210-213
2007
ISSN/ISBN: 0970-9290 PMID: 17938500 Document Number: 611076
Papillon-Lefevre syndrome is a rare autosomal recessive disorder in which there is palmoplantar keratinization and premature loss of both deciduous and permanent teeth. The palmoplantar keratoderma typically has its onset between the ages of 1 and 4 years and severe periodontitis starts at the age of 3 or 4 years. An early diagnosis of the syndrome can help preserve the teeth by early institution of treatment, using a multidisciplinary approach. We present two cases of the syndrome having all of the characteristic features.