Papillon-Lefèvre syndrome
Mahajan, V.K.; Thakur, N.S.; Sharma, N.L.
Indian Pediatrics 40(12): 1197-1200
2003
ISSN/ISBN: 0019-6061 PMID: 14722373 Document Number: 559076
Papillon- Lefèvre syndrome (PLS) is a rare autosomal recessive disorder of keratinization characterized by palmoplantar hyperkeratosis, periodontopathy and precocious loss of dentition. The exact pathomechanism of these clinical events mainly remains speculative. This paper describes two cases of PLS with classic clinical features and briefly review the relevant literature.
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