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Hereditary coagulation factor X deficiency

Kumar, A.; Mishra, K.L.; Kumar, A.; Mishra, D.

Indian Pediatrics 42(12): 1240-1242

2005

ISSN/ISBN: 0019-6061
PMID: 16424563
Document Number: 587014
Stuart Prower factor (Factor X) deficiency is a rare hereditary autosomal recessive coagulation disorder. We have come across three cases in the course of last 20 years at our institute. These patients presented with prolonged bleeding after minor trauma, epistaxis, subcutaneous bluish black nodules and two of them presented with history of consanguinity in parents. Hematological findings in correlation with clinical manifestations revealed severe factor X deficiency.

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