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Report 2 cases of congenital factor XII deficiency: a rare coagulation disorder

Kanjanapongkul, S.

Journal of the Medical Association of Thailand 94 Suppl. 3: S231-S232

2011

ISSN/ISBN: 0125-2208
PMID: 22043782
Document Number: 14647
Factor XII (F.XII, Hageman factor) is one of the contact system factors which initiates an intrinsic coagulation pathway. But its definite role is still unclear, because many cases of severe F.XII deficiency experience thrombotic events instead of a bleeding problem. Moreover most of them are asymptomatic. There have only been a few reports of F.XII deficiency in Thailand. The author reports two cases of congenital F.XII deficiency in Thai children.

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