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Gastrectomy in congenital factor VIi deficiency with substitution of factor VIi concentrate

Schricker, K.T.; Neidhardt, B.

Medizinische Klinik 76(19): 534-536

1981

ISSN/ISBN: 0025-8458
PMID: 7278798
Document Number: 181120
Case report of a 57-year old man, who had a severe congenital factor VII deficiency (factor VII 2%), and who was substituted with factor VII concentrate, before undergoing a subtotal gastrectomy. The patient was previously asymptomatic. The operation and wound-healing was without complication. That the patient, despite his factor VII deficiency, showed no clinical signs of a bleeding diathesis, raises the question, whether in such a case a factor VII substitution is necessary. 3 children of the patient (2 sons aged 25 and 23 years, and an 18 year old daughter) were examined and found to be heterozygote carriers to a degree of 32%, 42% and 60% factor VII; none showed sure signs of a bleeding tendency related to factor VII deficiency.

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