Febrile ulceronecrotic Mucha-Habermann disease with extensive skin necrosis in intertriginous areas
Yang, C.-C.; Lee, J.Y.-Y.; Chen, W.
European Journal of Dermatology Ejd 13(5): 493-496
2003
ISSN/ISBN: 1167-1122 PMID: 14693498 Document Number: 560784
Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a severe variant of pityriasis lichenoides et varioliformis acuta characterized by high fever and papulonecrotic skin lesions. Here we report a case of a 14-year-old boy with typical features of FUMHD and unusual manifestation of extensive skin necrosis in intertriginous regions including axillae, neck, inguinal and antecubital areas. Systemic administration of corticosteroid and erythromycin led to rapid healing of ulcerations without residual scar formation. Review of the literature showed male-predominance and favorable outcome in pediatric cases of FUMHD.