Budd-Chiari syndrome illustrated by four case reports
Grønbaek, H.; Nielsen, D.Tønner.; Astrup, L.Bording.
Ugeskrift for Laeger 164(25): 3360-3363
2002
ISSN/ISBN: 0041-5782 PMID: 12107952 Document Number: 546478
Budd-Chiari syndrome (BCS) represents obstruction of hepatic venous drainage. Patients with BCS must be managed individually, because the localisation of the obstruction, the cause, and natural history of the specific lesion differ between patients. We report four cases of Budd-Chiari syndrome where the first patient (who was protein C-deficient, took an oral contraceptive, and smoked) was successfully treated with transjugular intrahepatic portosystemic shunt (TIPS), the second patient (with polycythaemia vera) was treated with venesection and anticoagulation, the third patient underwent a successful liver transplantation. The last patient had a congenital vascular web and was treated by stenting.