Primary cardiac leiomyosarcoma originating from the pulmonary valve. Case report and review of the literature
Schröder, S.; Walker, T.; Greschniok, A.; Herdeg, C.; Karsch, K.R.; Ziemer, G.
Journal of Cardiovascular Surgery 42(1): 53-56
2001
ISSN/ISBN: 0021-9509 PMID: 11292906 Document Number: 532622
Primary cardiac tumours are rare findings (incidence 0.02% according to a recent meta-analysis) with dismal prognosis. Approximately 25% are malignant, mostly represented by sarcomas. Among these, leiomyosarcomas are exceptional. Treatment for primary cardiac leiomyosarcomas consists of radical surgical resection followed by adjuvant radiation therapy and/or chemotherapy. The mean survival after surgery and adjuvant therapies is 6.8 months. We present a rare case of a 40- year-old male patient with a primary cardiac leiomysarcoma originating from the pulmonary valve. This patient died after surgery and implantation of a homograft of the pulmonary trunk. Furthermore, the literature has been reviewed.