Dyskeratosis congenita associated with Hodgkin's disease
Baykal, C.; Büyükbabani, N.; Kavak, A.
European Journal of Dermatology Ejd 8(6): 385-387
1998
ISSN/ISBN: 1167-1122 PMID: 9729062 Document Number: 496905
Dyskeratosis congenita is a rare, hereditary, multisystem disorder characterized by mucocutaneous changes, pancytopenia and increased incidence of malignancy. Different types of neoplasia have been reported in association with dyskeratosis congenita. We present a second case associated with Hodgkin's disease. Delayed appearance of dermatological signs and association with chronic hepatitis B are other unusual features of this case.