Erdheim-Chester disease. Clinico-pathologic study of two cases
Farre, I.; Copin, M.C.; Boulanger, E.; Remy, J.; Wallaert, B.; Gosselin, B.
Annales de Pathologie 15(1): 59-62
1995
ISSN/ISBN: 0242-6498 PMID: 7702670 Document Number: 446840
Erdheim-Chester disease is a rare visceral xanthogranulomatosis characterized by bilateral, symmetrical sclerosis of the metaphyseal regions of long bones and infiltration of foamy, lipid-laden histiocytes. Clinically, it ranges from an asymptomatic, focal process to a fatal, systemic disease. We report two new cases, different in their presentation and extension.