Aortic dissection as complication of supravalvular aortic stenosis
Van Son, J.A.; Danielson, G.K.; Edwards, W.D.
Journal of Cardiovascular Surgery 35(5): 399-401
1994
ISSN/ISBN: 0021-9509 PMID: 7995831 Document Number: 426124
A 2-year-old patient with diffuse supravalvular aortic stenosis and the Williams-Beuren syndrome at autopsy was found to have dissection of the ascending aorta in addition to severe coronary artery disease and microfocal myocardial fibrosis. These findings emphasize the need for early surgical intervention in supravalvular aortic stenosis.
Document emailed within 1 workday
Related Documents
Seki, K.; Abe, T.; Kuribayashi, R.; Sekine, S.; Shibata, Y.; Yamagishi, I. 1994: Aortic dissection with giant pseudoaneurysm as a rare late complication of aortic valve replacement--a case report Nihon Kyobu Geka Gakkai 42(9): 1382-1387Christl, H. 1971: Supravalvular aortic stenosis in a swine Berliner und Munchener Tierarztliche Wochenschrift 84(24): 492
Morris, C.A. 1998: Genetic aspects of supravalvular aortic stenosis Current Opinion in Cardiology 13(3): 214-219
Apaydin, A.Z.; Posacioglu, H.; Nalbantgil, S.; Nart, D. 2004: Supravalvular aortic stenosis: repair with the Yacoub procedure Journal of Heart Valve Disease 13(6): 921-924
Masuhara, H.; Hiramatsu, T.; Harada, Y.; Hibino, N.; Honda, Y.; Satomi, G.; Yasukochi, S.; Matsui, H.; Otokozawa, K.; Kitamura, M.; Kajiyama, Y. 2004: Congenital supravalvular aortic stenosis; report of a case Kyobu Geka. Japanese Journal of Thoracic Surgery 57(12): 1135-1138
Del Fante, M.F.; Fossati, F.; Grande, A.; Ottino, G.M.; Santarelli, P. 1972: Supravalvular aortic stenosis. Surgical treatment of 4 cases Giornale Italiano di Cardiologia 2(4): 507-518
Santarelli, P.; Grande, A.; Possati, F.; Rispoli, P.; Gobbi, G.; Catania, G.; Bergui, G.C.; Lino, R. 1977: Supravalvular aortic stenosis. Apropos of 4 familial cases Minerva Cardioangiologica 25(9): 675-686
Doty, D.B.; Eastham, C.L.; Hiratzka, L.F.; Wright, C.B.; Marcus, M.L. 1982: Determination of coronary reserve in patients with supravalvular aortic stenosis Circulation 66(2 Part 2): I186-I192
Dumont, C.R.; Gil, M.; Mispireta, J.; Attié, F. 1975: Supravalvular aortic stenosis. Report of clinical findings in 5 patients Archivos del Instituto de Cardiologia de Mexico 45(2): 151-163
Chehab, G.; Darido, J.; El-Rassi, I.; Gerbaka, B.; Smayra, T.; Saliba, Z. 2015: Supravalvular aortic stenosis with and without coronary lesions in pediatrics. a Lebanese study Le Journal Medical Libanais. Lebanese Medical Journal 63(2): 81-86
Gourgon, R.; Wayneberger, M.; Bourthoumieux, A.; Brusset, P.; Legrand, M.; Langlois 1970: Double congenital aortic stenosis, supravalvular cushion-like and subvalvular diaphragm-like Archives des Maladies du Coeur et des Vaisseaux 63(12): 1773-1783
Osumi, M.; Matsueda, T.; Kurushima, A.; Otani, T.; Fukumura, Y. 2010: Aortic dissection after aortic valve replacement for bicuspid aortic valve complicated with ascending aortic dilatation; report of a case Kyobu Geka. Japanese Journal of Thoracic Surgery 63(3): 237-240
Tedoriya, T.; Kawasuji, M.; Sakakibara, N.; Hirano, K.; Watanabe, Y.; Iwa, T. 1991: The use of Doty's extended aortoplasty in binovular twins with congenital supravalvular aortic stenosis Nihon Kyobu Geka Gakkai 39(11): 2092-2095
Vogt, J.; Rupprath, G.; Grimm, T. 1980: Qualitative and quantitative investigations in supravalvular aortic stenosis by cross-sectional echocardiography Zeitschrift für Kardiologie 69(1): 70-73
Tanaka, H.; Ajiki, H.; Iwashiro, K.; Nakamura, K.; Baba, M.; Takeda, H.; Asai, Y.; Komatsu, S.; Sawada, Y.; Tomita, H. 1992: A case report of patch aortoplasty for supravalvular aortic stenosis associated with Williams syndrome Kyobu Geka. Japanese Journal of Thoracic Surgery 45(2): 156-158
Forman, M.B.; Kinsley, R.H.; Du Plessis, J.P.; Dansky, R.; Milner, S.; Levin, S.E. 1982: Surgical correction of combined supravalvular and valvular aortic stenosis in homozygous familial hypercholesterolaemia South African Medical Journal 61(16): 579-582
Yokoyama, Y.; Nagashima, M.; Satoh, H.; Hori, T.; Nakata, T.; Saito, H.; Seike, Y.; Tomino, T. 2005: Successful repair of supravalvular aortic stenosis using Steinberg 3 sinuses reconstruction; report of a case Kyobu Geka. Japanese Journal of Thoracic Surgery 58(7): 569-572
Marla, R.; Woods, T.; Lilly, R.Eric.; Nicolosi, A.C.; Masroor, S. 2009: Supravalvular aortic membrane with severe aortic regurgitation: an unusual presentation in adults Journal of Heart Valve Disease 18(3): 347-348
Komooka, M.; Higashiue, S.; Matsubayashi, K.; Tonda, H.; Hiramatsu, N.; Furuya, O. 2014: Retrograde Stanford type A aortic dissection treated by thoracic endo-vascular aortic repair (TEVAR) after ascending aortic replacement Kyobu Geka. Japanese Journal of Thoracic Surgery 67(2): 109-112
Marni, E. 1974: On a case of aortic supravalvular stenosis, elfish facies and mental deficiency. So-called Beuren's syndrome Minerva Pediatrica 26(40): 2005-2012