Supravalvular aortic membrane with severe aortic regurgitation: an unusual presentation in adults
Marla, R.; Woods, T.; Lilly, R.Eric.; Nicolosi, A.C.; Masroor, S.
Journal of Heart Valve Disease 18(3): 347-348
2009
ISSN/ISBN: 0966-8519 PMID: 19557996 Document Number: 634110
Aortic stenosis due to supravalvular membrane usually presents in children. It may be associated with fusion of the left coronary leaflet and the supravalvular membrane, causing obstruction of the left coronary ostium, and resulting in myocardial ischemia. Despite the immobilization of the left coronary leaflet, these patients present in childhood with aortic stenosis and not regurgitation, with or without accompanying myocardial ischemia. The case is described of an adult patient with supravalvular aortic membrane presenting with severe aortic regurgitation and myocardial infarction due to fusion of the left coronary leaflet with the supravalvular membrane.