Successful repair of supravalvular aortic stenosis using Steinberg 3 sinuses reconstruction; report of a case
Yokoyama, Y.; Nagashima, M.; Satoh, H.; Hori, T.; Nakata, T.; Saito, H.; Seike, Y.; Tomino, T.
Kyobu Geka. Japanese Journal of Thoracic Surgery 58(7): 569-572
2005
ISSN/ISBN: 0021-5252 PMID: 16004340 Document Number: 591208
Steinberg method is a modification of Doty extended aortoplasty for supravalvular aortic stenosis (SAS). This modification entails placement of an additional patch in the left coronary sinus. A 3-year-old boy was diagnosed as SAS with aortic valvular stenosis. He was noticed a systolic murmur from 1 month after his birth. Echocardiography showed left ventricular hypertrophy, and pressure gradient of 80 mmHg was measured between the ascending aorta and the left ventricle. Cardiac catheterization revealed severe aortic stenosis at the sino-tubular (ST) junction. We adopted Steinberg 3 sinuses reconstruction. After this operation, there was no pressure gradient at ST junction although aortic valvular stenosis remained and mild aortic valve regurgitation newly developed. As this method can produce a symmetric aortic root, it may reduce aortic valve deformity especially on the left coronary cusp.