Michel's anomaly, type i microtia and microdontia
Hersh, J.H.; Ganzel, T.M.; Fellows, R.A.
Ear Nose and Throat Journal 70(3): 155-157
1991
ISSN/ISBN: 0145-5613 PMID: 2044484 Document Number: 382458
Michel's anomaly is an extremely rare cause of congenital sensorineural hearing loss. We present a 2-1/2 year old white female with this inner ear defect associated with type I microtia and microdontia. Assessment of anatomic structures of the ear is critical in an infant with abnormal auditory brainstem responses to determine whether a structural lesion is present and the most appropriate rehabilitative approach available.