Acute intermittent porphyria and the Klüver -- Bucy syndrome
Guidotti, T.L.; Charness, M.E.; Lamon, J.M.
Johns Hopkins Medical Journal 145(6): 233-235
1979
ISSN/ISBN: 0021-7263 PMID: 513431 Document Number: 3738
Acute intermittent porphyria is frequently associated with transient neurologic complications and is occasionally associated with serious permanent disability; the related neurologic conditions range from uncomfortable neuropathies to suicidal depression. We have not found a previous report of acute intermittent porphyria as a possible cause of the Kluver- Bucy syndrome. The association merits recognition because the syndrome usually implies a grave prognosis with extensive structural injury to the brain. In this case both the usual complications of acute intermittent porphyria and this uncommon neurologic syndrome were reversible.
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