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Cystic fibrosis in infants revealed by severe respiratory distress. Mid-term course

Sardet, A.; Couvreur, J.; Costil, J.; Just, J.; Boule, M.; Tournier, G.

Archives Francaises de Pediatrie 47(9): 653-656

1990

ISSN/ISBN: 0003-9764
PMID: 2078125
Document Number: 356162
We report the follow-up of 13 infants aged 2.5 to 24 months in whom cystic fibrosis disease presented as respiratory distress. All infants received an intensive treatment. Mean clinical, radiological and microbiological follow-up was 3.1 years. Ten children aged 1.5 to 8.5 years are still alive. One of them presents with serious respiratory failure, with a Shwachman score of 50. The Shwachman score is between 85 and 70 for 8 of 13 and 65 for one. The prognosis of this group did not differ from the one usually observed in the disease. It depends partially on early intensive care management and is not altered by mechanical ventilation.

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Chevalier, J.Y.; Costil, J. 1992: Extracorporeal membrane oxygenation: is it possible to better the prognosis of severe respiratory distress in infants? Annales de Pediatrie 39(10): 608-610
Charon, A.; Taeusch, W.; Fitzgibbon, C.; Smith, G.B.; Treves, S.T.; Phelps, D.S. 1989: Factors associated with surfactant treatment response in infants with severe respiratory distress syndrome Pediatrics 83(3): 348-354
Vivanco, G.; Cuellar, A.; Antelo, O.; Ceruti, E. 1979: Cystic fibrosis of the pancreas. Clinical, laboratory and respiratory function tests. Long-term follow-up Revista Chilena de Pediatria 50(4): 6-16
Marraro, G.; Foresti, B.; Casiraghi, G.; Monici Preti, P. 1991: Follow-up on infants treated with porcine surfactant replacement for severe neonatal and infant respiratory distress syndrome: antigenic reactivity evaluation Drugs under Experimental and Clinical Research 17(10-11): 511-515
Farrell, P.M.; Blackburn, G.K.; Cefalo, R.C. 1979: Familial respiratory distress syndrome in three consecutive full-term infants. Case reports and documentation of lung enzyme activities Journal of Reproductive Medicine 22(5): 255-258
Smith, J.; van Lierde, S.; Devlieger, H.; Daniels, H.; Eggermont, E. 1995: Birth weight and early lung compliance as predictors of short-term outcome in premature infants with respiratory distress syndrome South African Medical Journal 85(11): 1157-1160
Croft, P.R.; Racz, M.I.; Bloch, J.D.; Palmer, C.H. 2005: Autopsy confirmation of severe pulmonary interstitial fibrosis secondary to Munchausen syndrome presenting as cystic fibrosis Journal of Forensic Sciences 50(5): 1194-1198
Nesić, S.; Janjić, M.; Kovacević, D.; Leposavić, M.; Rakojković, M. 1982: Pathologicomorphological changes in the lungs of premature infants who died of acute respiratory insufficiency caused by the respiratory distress syndrome Srpski Arhiv Za Celokupno Lekarstvo 110(1): 1-7
Tirouvanziam, R.; Desternes, M.; Saari, A.; Puchelle, E.; Péault, B.; Chinet, T. 1998: Bioelectric properties of human cystic fibrosis and non-cystic fibrosis fetal tracheal xenografts in SCID mice American Journal of Physiology 274(4): C875-C882
Denter, M.; Ramsay, M.; Jenkins, T. 1992: Cystic fibrosis. Part I. Frequency of the delta F508 mutation in South African families with cystic fibrosis South African Medical Journal 82(1): 7-10
Paranka, M.S.; Clark, R.H.; Yoder, B.A.; Null, D.M. 1995: Predictors of failure of high-frequency oscillatory ventilation in term infants with severe respiratory failure Pediatrics 95(3): 400-404
1976: Screening newborn infants for cystic fibrosis Medical Letter on Drugs and Therapeutics 18(8): 35-36
Warwick, W.J. 1972: Cystic fibrosis. Screen newborn infants Minnesota Medicine 55(11): 1025-1026
Wang, M.C.; Shu, S.G.; Chang, S.M.; Ho, W.L.; Chi, C.S. 1993: Cystic fibrosis in two Chinese infants in Taiwan Zhonghua Minguo Xiao Er Ke Yi Xue Hui Za Zhi Zhonghua Minguo Xiao Er Ke Yi Xue Hui 34(4): 314-321
Lloyd-Still, J.D.; Powers, C. 1990: Carnitine metabolites in infants with cystic fibrosis Acta Universitatis Carolinae. Medica 36(1-4): 78-80
Cheng, S-Lung.; Wang, H-Chien.; Yang, P-Chyr. 2005: Acute respiratory distress syndrome and lung fibrosis after ingestion of a high dose of ortho-phenylphenol Journal of the Formosan Medical Association 104(8): 585-587
Ashitani, J.; Mukae, H.; Ihiboshi, H.; Hiratsuka, T.; Taniguchi, H.; Mashimoto, H.; Matsukura, S. 1997: Serum-soluble adhesion molecules in patients with idiopathic pulmonary fibrosis and acute respiratory distress syndrome Nihon Kyobu Shikkan Gakkai Zasshi 35(9): 942-947
Torstenson, O.L.; Humphrey, G.B.; Edson, J.R.; Warwick, W.J. 1970: Cystic fibrosis presenting with severe hemorrhage due to vitamin K malabsorption: a report of three cases Pediatrics 45(5): 857-861
Egan, E.A. 1992: Synthetic surfactants in infants with respiratory distress syndrome New England Journal of Medicine 326(25): 1704; Author Reply 1704-1705
Saintonge, J. 1991: Respiratory distress in newborn infants: diagnostic approach Pediatrie 46(5): 411-416