Steinert's disease and conduction disorders. Apropos of a familial study
Maloisel, F.; Wolff, F.; Chauvin, M.; Zimmerman, C.; Brechenmacher, C.
Annales de Cardiologie et d'Angeiologie 37(7): 357-360
1988
ISSN/ISBN: 0003-3928 PMID: 3064691 Document Number: 319774
The authors reported a new family case of Steinert with twelve years follow-up. The study of potentials in the bundle of his was performed in all patients, showed an intra- and infra-hisian blocks. This study showed a discrepancy between muscular and myocardial evolutive injury, a very important knowledge for follow-up. Conduction disturbances were found in two cases and pacemaker insertion was performed in one patient. The authors specified the indication of electrophysiological studies during the onset and pacemaker implantation in all patient with a typical or suggestive history of syncope.