Congenital generalized lipodystrophy. Lipid changes. Therapeutic trials
Lestradet, C.; Massol, J.; Plouvier, E.; Narboni, G.; Raffi, A.
Archives Francaises de Pediatrie 42(8): 705-707
1985
ISSN/ISBN: 0003-9764 PMID: 4074100 Document Number: 259606
On the occasion of a new case of congenital generalized lipodystrophy the clinical features of this disease are reviewed. Furthermore, the frequent association of type V hypertriglyceridemia is emphasized. Various pathogenic hypotheses guide the therapeutic attempts, which are often unsuccessful.