Neurofibroma and neurofibrosarcoma in Recklinghausen's neurofibromatosis
Von Gumppenberg, S.; Karpf, P.M.; Prokscha, G.W.; Kramann, B.; Neher, G.
Fortschritte der Medizin 96(31): 1563-1568
1978
ISSN/ISBN: 0015-8178 PMID: 97194 Document Number: 128650
The neurofibromatosis von Recklinghausen is a systemic disease, which can cause various different changes in the body. The case report of a female patient shows all the typical signs of neurofibromatosis von Recklinghausen. These signs are café-au-lait spots, congenital tibia pseudarthrosis, abdominal plexiform neurofibromatosis and peripherical neurofibromas with sarcomatous degeneration.