Excess C-26 fatty acid in cultured skin fibroblasts from adrenoleukodystrophy and adrenomyeloneuropathy patients
Kawamura, N.; Moser, H.W.; Kishimoto, Y.; Schaumburg, H.; Suzuki, K.; Murphy, J.
Transactions of the American Neurological Association 103: 113-115
1978
ISSN/ISBN: 0065-9479 PMID: 757032 Document Number: 125193
Document emailed within 1 workday
Related Documents
Assies, J.; Haverkort, E.B.; Lieverse, R.; Vreken, P. 2003: Effect of dehydroepiandrosterone (DHEA) supplementation on fatty acid and hormone levels in patients with X-linked adrenoleukodystrophy Advances in Experimental Medicine and Biology 544: 243-244Raederstorff, D.; Loechleiter, V.; Moser, U. 1995: Polyunsaturated fatty acid metabolism of human skin fibroblasts during cellular aging International Journal for Vitamin and Nutrition Research. Internationale Zeitschrift für Vitamin- und Ernahrungsforschung. Journal International de Vitaminologie et de Nutrition 65(1): 51-55
Schutgens, R.B.; Bouman, I.W.; Nijenhuis, A.A.; Wanders, R.J.; Frumau, M.E. 1993: Profiles of very-long-chain fatty acids in plasma, fibroblasts, and blood cells in Zellweger syndrome, X-linked adrenoleukodystrophy, and rhizomelic chondrodysplasia punctata Clinical Chemistry 39(8): 1632-1637
Kraus, I.; Antonowicz, I.; Shah, H.; Lazarus, H.; Shwachman, H. 1971: Metachromasia and assay for lysosomal enzymes in skin fibroblasts cultured from patients with cystic fibrosis and controls Pediatrics 47(6): 1010-1018
Kopelovich, L.; DeLeo, A.B. 1986: Elevated levels of p53 antigen in cultured skin fibroblasts from patients with hereditary adenocarcinoma of the colon and rectum and its relevance to oncogenic mechanisms Journal of the National Cancer Institute 77(6): 1241-1246
Vogel, K.G.; Clark, P.E. 1989: Small proteoglycan synthesis by skin fibroblasts cultured from elderly donors and patients with defined defects in types i and IIi collagen metabolism European Journal of Cell Biology 49(2): 236-243
Saito, E.; Yoshimoto, Y.; Oshima, H.; Yoshida, H.; Kinoshita, M. 1989: Fluorescent antibodies in polymyositis using cultured human skin fibroblasts: granular perinuclear cytoplasmic staining pattern by sera from patients with polymyositis and pulmonary fibrosis Journal of Rheumatology 16(1): 47-54
DeWailly, D.; Maes, M.; Amrhein, J.A.; Rothwell, S.W.; Migeon, C.J. 1979: Antibody method for measurement of dihydrotestosterone receptors in cultured human skin fibroblasts Journal of Laboratory and Clinical Medicine 94(1): 106-113
Charbonne, F.; Rousseau, P.; Malpuech, G.; Geneix, A. 1980: Tay-Sachs disease: a case report. Interest of ultrastructural studies of cultured skin fibroblasts Archives Francaises de Pediatrie 37(1): 51-53
Naito, E.; Toshima, K.; Kuroda, Y.; Takeda, E.; Miyao, M. 1986: Diagnosis of pyruvate dehydrogenase complex deficiency in biopsied muscles and cultured skin fibroblasts No to Hattatsu 18(6): 459-463
Chiu, H.C.; Wu, Y.C.; Lu, Y.C. 1987: Effect of dextran sulfate on the growth of cultured fibroblasts derived from normal human skin and keloid lesions Journal of the Formosan Medical Association 86(3): 264-270
Yoshida, K.; Takeda, S.; Shoji, S.; Yanagisawa, N.; Yatani, R. 1988: An adult case of Cockayne syndrome with protracted clinical course--a study of ultraviolet irradiation test using cultured skin fibroblasts Rinsho Shinkeigaku 28(6): 609-615
Brown, F.R.; Van Duyn, M.A.; Moser, A.B.; Schulman, J.D.; Rizzo, W.B.; Snyder, R.D.; Murphy, J.V.; Kamoshita, S.; Migeon, C.J.; Moser, H.W. 1982: Adrenoleukodystrophy: effects of dietary restriction of very long chain fatty acids and of administration of carnitine and clofibrate on clinical status and plasma fatty acids Johns Hopkins Medical Journal 151(4): 164-172
Hansbrough, J.F.; Cooper, M.L.; Cohen, R.; Spielvogel, R.; Greenleaf, G.; Bartel, R.L.; Naughton, G. 1992: Evaluation of a biodegradable matrix containing cultured human fibroblasts as a dermal replacement beneath meshed skin grafts on athymic mice Surgery 111(4): 438-446
Wang, L.; Teng, W.; Shan, Z. 2000: Effect of IFN-gamma, IL-4 on proliferation and synthesis of hyaluronic acid and collagen in cultured human retroorbital fibroblasts in vitro Chinese Medical Journal 113(10): 907-910
Tyrrell, R.M.; Pidoux, M. 1986: Quantitative differences in host cell reactivation of ultraviolet-damaged virus in human skin fibroblasts and epidermal keratinocytes cultured from the same foreskin biopsy Cancer Research 46(6): 2665-2669
Cooper, M.L.; Hansbrough, J.F. 1991: Use of a composite skin graft composed of cultured human keratinocytes and fibroblasts and a collagen-GAG matrix to cover full-thickness wounds on athymic mice Surgery 109(2): 198-207
Hollenberg, M.D. 1977: Steroid-stimulated amino acid uptake in cultured human fibroblasts reflects glucocorticoid and anti-inflammatory potency Molecular Pharmacology 13(1): 150-160
Sultan, C.; Coupé, M.; Devillier, C.; Chavis, C.; Terraza, A.; Descomps, B. 1983: Metabolism of dihydrotestosterone in cultured skin fibroblasts: reduction to 5 alpha-androstane-3 alpha, 17 beta-diol Comptes Rendus des Seances de la Societe de Biologie et de ses Filiales 177(1): 83-92
Becker, Y.; Tabor, E. 1989: Skin fibroblasts from patients with the genetic disorder hereditary hemorrhagic telangiectasia compared with ataxia-telangiectasia fibroblasts in their response to the radiomimetic drug neocarzinostatin Israel Journal of Medical Sciences 25(2): 81-86