Radiological and angiocardiographical aspects of primary endocardial fibroelastosis in children
Azcuna, J.I.; Cabrera, A.; Chouza, M.; Bilbao, F.; Pastor, E.; Oñate Landa, A.
Anales Espanoles de Pediatria 9(4): 364-372
1976
ISSN/ISBN: 0302-4342 PMID: 984598 Document Number: 106721
In this article we try to show the value of radiography and angiocardiography in primary endocardial fibroelastosis. The 20 CASEs studied in this report, were angiocardiographically and/or necropsically proved. In spite of different opinions, we think that it is possible to reach an approximate diagnosis of this condition if we use the clinical and angiohemodinamic examinations. On the other hand, it is necessary to point out that pathology is characteristic. The most important radiological signs were cardiomegaly, together with venocapilar congestion, both of variable magnitude, and dependent on the degree of cardiac insufficiency. By means of angiocardiography we could appreciate a great dilatation and hypertrophy of the left ventricle and a reduction of the mobility and distensibility of this cavity along the cardiac cycle.