Echocardiographic findings and function analysis of the left ventricle in infants with endocardial fibroelastosis
Schmaltz, A.A.; Heil, R.P.; Steil, E.; Brown, D.J.; Apitz, J.
Zeitschrift für Kardiologie 68(8): 547-550
1979
ISSN/ISBN: 0300-5860 PMID: 506364 Document Number: 149462
7 infants with the clinical picture and the typical hemodynamic and angiocardiographic findings of endocardial fibroelastosis were studied echocardiographically. The echocardiograms were digitized and analyzed by the method of Gibson and Brown and compared with those of 8 normal infants. The echoes of EFE-patients showed a nearly twice as large LV-diameter. The mitral valve was displaced posteriorly, the septal motion in 4 of them abnormal. The shortening fraction was significantly reduced, the LPEP/LVET quotient increased. The comparison of LPEP with the Q to mitral valve closing interval revealed a considerable prolongation of isovolumetric contraction time. The result of computer analysis was a decrease of peak Vcf and maximum lengthening rate. The echocardiographic pattern is typical but not pathognomonic, it gives no prognostic information.