Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) : a case report in Thailand
Manop, J.; Chamnanvanakij, S.; Wattanasarn, C.
Journal of the Medical Association of Thailand 87(11): 1385-1388
2004
ISSN/ISBN: 0125-2208 PMID: 15825718 Document Number: 9341
Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is a rare congenital disease with high mortality rate. The authors report a case of a female term infant with massive abdominal distension at birth. Abdominal ultrasonography revealed a huge cystic mass resolved after urinary catheterization. Exploratory laparotomy was performed and intraoperative findings were an enlarged urinary bladder, microcolon, short bowel and malrotation of the small intestine. Ladd's procedure, ileostomy and vesicostomy were performed. Pathological findings of rectal biopsy revealed normal ganglion cells. Although prokinetic drugs were given for promoting bowel motility, enteral feedings were not tolerated. She died from septicemia at the age of 50 days.
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