Idiopathic Atypical Haemolytic Uraemic Syndrome presenting with acute dystonia
Rizwan, M.; Maduemem, K.E.
Irish Medical Journal 110(7): 622
2017
ISSN/ISBN: 0332-3102 PMID: 29169004 Document Number: 694313
Hemolytic Uremic Syndrome (HUS), a triad of microangiopathic hemolytic anemia, thrombocytopenia and acute kidney injury. The atypical HUS (aHUS) results from over activation of complement system with formation of micro thrombi and damage to endothelial cells resulting in renal impairment in 50 % and death in 25 %, commonly in untreated patients. We report an intriguing case of aHUS presenting with acute onset of movement disorder and fluctuating delirium.