Retroperitoneal primitive neuroectodermal tumor (PNET) : case report and review of literature
Koch, A.; Frigo, S.; Lecointre, L.; Hummel, M.; Akladios, C.Y.; Bergerat, J.P.; Noël, G.; Wattiez, A.
European Journal of Gynaecological Oncology 38(2): 314-318
2017
ISSN/ISBN: 0392-2936 PMID: 29953804 Document Number: 693199
Primitive Neuroectodermal tumor belongs to the family of Ewing's tumor and is characterized by at (11;22) (q24;ql2) or at (21;22) (q22;ql2) translocation. Retroperitoneal primitive neuroectodermal tumor (PNET) are rare, usually affect young adults, and are often diagnosed late. There is no specific characteristics for imaging. The diagnosis is made on histological examination of the surgical spec- imen or biopsies. Radiotherapy and chemotherapy complete the treatment. The authors report the case of a 26-year-old patient who only had pelvic discomfort. Diagnostic laparoscopy showed a retroperitoneal and retrovesical mass of five centimeters. The patient benefited from adjuvant chemotherapy and radiotherapy. She is free of disease 30 months after treatment.