Duchenne Muscle Dystrophy Caused Bronchial Obstruction
Fujiwara, A.; Iwashiro, N.; Ohara, M.
Kyobu Geka. Japanese Journal of Thoracic Surgery 70(4): 313-315
2017
ISSN/ISBN: 0021-5252 PMID: 28428530 Document Number: 691495
Duchenne muscle dystrophy (DMD), X-linked recessive genetic disorder, causes a variety of complications including scoliosis. We report a case of bronchial obstruction and hemorrhage caused by scoliosis with DMD. A man in his forties having been hospitalized due to DMD since the age of 6, produced bloody sputum. A chest X-ray showed atelectasis in his right lower lung. A computed tomography and bronchoscopy indicated that scoliosis and thoracic deformity due to muscle dystrophy caused compression of a right main bronchus by the vertebra, leading to bronchial obstruction and bleeding. We decided to follow closely without therapy because the bleeding had stopped as of the bronchoscopy. A high-risk surgery or bronchial stenting may be needed if he presents with severe bleeding or infection.