What prognosis for Ebstein's anomaly without surgery? Hassan Ii teaching hospital experience
Garba, M.; Atmani, S.; Sani, R.; Nouhou, K.A.
La Tunisie Medicale 94(4): 284-289
2016
ISSN/ISBN: 0041-4131 PMID: 27704512 Document Number: 688087
Background From the first description in 1886, significant progress was made on the treatment of Ebstein disease by mono and bi-ventricular surgery. Aim To highlight the prognosis of Ebstein's anomaly in the pediatric department of Hassan II hospital in Fez. Methods This is a descriptive and retrospective study of 4 years. Results We collected nine patients (seven boys and two girls) with a mean age of 5.3 years. Cyanosis was the main mode of revelation of the disease. In three patients Ebstein's anomaly was part of a malformative syndrome. All patients had only symptomatic medical treatment. Five patients are still alive at a follow up of one to six years. Conclusion Symptomatic medical treatment of Ebstein malformation may improve the prognosis of the disease.
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