Surgical Repair of Ebstein's Anomaly in the Adult
Kasahara, S.
Kyobu Geka. Japanese Journal of Thoracic Surgery 72(4): 283-289
2019
ISSN/ISBN: 0021-5252 PMID: 31266914 Document Number: 698013
Ebstein's anomaly (EA) is a rare congenital cardiac malformation and this anomaly is a disorder of a tricuspid valve development in which the valve leaflets fail to delaminate properly from the ventricular wall. Clinical symptoms are age dependent and include cyanosis (size of inter-atrial communication), right-sided heart failure, arrhythmias, and general fatigue on exercise. Optimal timing of surgical intervention is often difficult and must be individualized. Patients have good long-term survival and functional outcomes after undergoing surgery for Ebstein's anomaly in adult population. Operation includes tricuspid valve repair or replacement, closure of any inter-atrial communications, and appropriate antiarrhythmia procedures.