Non-Clonal Mast Cell Activation Syndrome: Description of Series of Patients, Diagnostic Criteria and Treatment
Confino-Cohen, R.; Mekori, Y.A.
Harefuah 154(8): 507-9 540
2015
ISSN/ISBN: 0017-7768 PMID: 26480615 Document Number: 683932
A non-clonal mast cell activation syndrome is a newly emerged diagnosis. It shares the clinical features of anaphylaxis and mastocytosis despite having distinct mast cell biology. In this,paper we describe a series of patients representing the spectrum of non-clonal mast cell activation syndrome (nc-MCAS). We highlight the clinical manifestations of nc-MCAS as well as the diagnostic criteria and treatment options.
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