Familial congenital hepatic fibrosis: report of a family with three affected children
Farahmand, F.; Soleimani, K.; Hashemi, M.; Shafieyoun, A.; Rezaei, N.; Yousefi, A.
Acta Medica Iranica 51(9): 655-656
2013
ISSN/ISBN: 0044-6025 PMID: 24338199 Document Number: 669761
Congenital hepatic fibrosis (CHF) is a developmental disorder of the biliary system, characterized by defective remodeling of the ductal plate. Herein a family of three children, from consanguineous parents, with minor thalassemia is presented who suffered from congenital hepatic fibrosis (CHF). Prompt diagnosis and appropriate treatment are necessary to avoid further complications in the affected patients.