Resection of a giant malignant mediastinal peripheral nerve sheath tumour under cardiopulmonary bypass
Su, J.W.; Chua, Y.L.; Ong, B.H.; Lim, C.H.
Singapore Medical Journal 50(6): e199-e200
2009
ISSN/ISBN: 0037-5675 PMID: 19551295 Document Number: 635667
Malignant peripheral nerve sheath tumour (MPNST) is a rare occurrence in the mediastinum. It is biologically aggressive and is generally resistant to chemoradiation therapy. The mainstay of treatment is complete surgical resection. We report a large MPNST which invaded into the adjacent aortic wall in a 50-year-old man. Extensive resection, which included aortic reconstruction under cardiopulmonary bypass and deep hypothermic arrest, was necessary for a good long-term outcome.