Aortic root reconstruction in a nine-year-old child: a case report
Szabolcs, Z.; Hüttl, T.; Szudi, L.; Bartha, E.; Veres, G.; Balázs, Görgy.; Hartyánszky, I.
Journal of Heart Valve Disease 18(2): 220-222
2009
ISSN/ISBN: 0966-8519 PMID: 19455899 Document Number: 632313
Aortic root dilatation is present by the age of five years in approximately 35% of patients suffering from Marfan syndrome. However, children rarely undergo surgery for aortic aneurysm and aortic regurgitation during their first decade of life. A nine-year-old boy, who presented with severe aortic regurgitation associated with a 76.8 mm aneurysm of the ascending aorta, underwent a Bentall procedure. Since the aortic annulus was markedly dilated and the cusps were structurally abnormal, the aortic valve was not spared.