Supernumerary nipples in association with Hailey-Hailey disease in a Tunisian family
Benmously-Mlika, R.; Deghais, S.; Bchetnia, M.; Charfeddine, C.; Mokni, M.; Kassar, S.; Haouet, S.; Boubaker, S.; Mokhtar, I.; Abdelhak, S.; Dhahri, A.Ben.Osman.
Dermatology Online Journal 14(6): 15
2008
ISSN/ISBN: 1087-2108 PMID: 18713596 Document Number: 615780
Supernumerary nipples (SNs) or polythelia are developmental abnormalities of breast tissue. They are located along the embryonic mammary lines. Polythelia usually occurs as a sporadic abnormality, although familial aggregation has been occasionally reported. Hailey-Hailey disease is a rare autosomal genodermatosis characterized by disturbed keratinocyte adhesion. These cutaneous disorders have been described in correlation with many other abnormalities. We report here the association of Hailey-Hailey disease and supernumerary nipples in a Northern Tunisian family. To our knowledge, this is the first report of such a clinical association.