Pulmonary blastoma in adults
Terrettaz, E.; Frey, J.-G.; Chavaillaz, O.
Revue Medicale Suisse 3(99): 470
2007
ISSN/ISBN: 1660-9379 PMID: 17424798 Document Number: 614835
Pneumoblastoma (PB) is a rare, malignant, primary, pulmonary tumour, of young adults. Its discovery is fortuitous in asymptomatic patients. It is a well-delimited, homogeneous lesion in the lung periphery. Histologically, its structure looks like a normal fetal lung. The surgical resection is the treatment of choice. The radiotherapy is an empirical palliative treatment to relieve dyspnea when other treatments failed. The prognosis is bad: 16% survive 5 years and 8% beyond 10 years, all treatments included. Metastases could appear in the liver, the brain and the bone.