Benign lipoblastomalike tumor of the vulva: report of a case affecting a young patient
Atallah, D.; Rouzier, R.; Chamoun, M.Laurence.; Mansour, F.; Nabaa, T.; Chababi, M.; Duvillard, P.; Chahine, G.
Journal of Reproductive Medicine 52(3): 223-224
2007
ISSN/ISBN: 0024-7758 PMID: 17465291 Document Number: 613439
BACKGROUND: Mesenchymal vulvar tumors are rare, and a benign lipoblastomalike tumor may be confused with malignancy.CASE: A 15-year-old patient consulted for a right labium tumefaction measuring 15 cm. After excision, histologic examination revealed a well-circumscribed and tabulated tumor. The lobules were composed of slender spindle cells showing slightly eosinophilic cytoplasm with indistinct boundaries, uniform nuclei with finely granular chromatin and no nucleoli. Scattered Signet-ring-type lipoblasts were observed. The background was myxoid, with a "chickenwire" capillary vascular network mimicking a myxoid liposarcoma. No mitotic figures, necrosis or pleomorphism was noted.CONCLUSION. This mesenchymal tumor had adipocytic differentiation and no patent sign of malignancy, akin to infantile lipoblastoma. Because of the benign behavior of this tumor, complete excision without radiation is recommended.