Epidermolysis bullosa pruriginosa: a rare autosomal dominant variant
Das, S.; Roy, A.K.; Kar, C.; Giri, P.P.
Journal of the Indian Medical Association 105(7): 388; 390
2007
ISSN/ISBN: 0019-5847 PMID: 18178992 Document Number: 610389
A 35 years female presented with extremely pruritic, violaceous, small vesiculopapular lesions over both shins since 11/12 years of age. The intensity of pruritus slightly descreased following oozing of fluid. History of similar incidence in her mother and maternal grandfather was present. There was no toe-nail dystrophy. Histopathology report showed the lesions had hyperkeratotic, mild acanthosis, dermal lymphohistiocytic infiltrate and subepidermal cleft. The case was diagnosed to be a case of epidermolysis bullosa pruriginosa.