Wounds in children and Epidermolysis bullosa
Pustisek, N.; Babić, I.; Kljenak, A.; Striber, N.; Visnjić, S.; Ilić, M.K.
Acta Medica Croatica Casopis Hravatske Akademije Medicinskih Znanosti 66(Suppl 1): 119-122
2012
ISSN/ISBN: 1330-0164 PMID: 23193833 Document Number: 658861
Epidermolysis bullosa is a group of inherited disorders characterized by blister formation on the skin and mucous membrane as the result of molecular defects in genes coding for different structural proteins. They present with a wide clinical spectrum of manifestations because of a variety of molecular defects. Therapy depends on the form of the disease, severity and extent of skin involvement and extracutaneous manifestations, and consists of supportive skin care and supportive care for other organ systems. Skin care includes protection against trauma, proper skin care, treatment of blisters and erosions, and regular dermatological controls for early detection of skin cancer.