Congenital intrahepatic porto-systemic venous shunt with galactosemia
Sodhi, K.S.; Thapa, B.R.; Walia, A.; Khandelwal, N.
Indian Journal of Gastroenterology Official Journal of the Indian Society of Gastroenterology 26(2): 87-88
2007
ISSN/ISBN: 0254-8860 PMID: 17558073 Document Number: 609191
We report a 51-day-old infant with congenital intrahepatic porto-systemic venous shunt associated with galactosemia, who presented with cholestatic jaundice. He was treated with ursodeoxycholic acid, calcium supplements and galactose-free diet. The child was asymptomatic six weeks later.
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