ANCA-negative limited Wegener's granulomatosis
Ghosh, A.; Bandyopadhyay, D.; Basu, S.; Majumdar, A.; Dutta, S.
Indian Journal of Dermatology Venereology and Leprology 70(2): 102-104
2004
ISSN/ISBN: 0973-3922 PMID: 17642576 Document Number: 580753
A 26-year-old man presented with epistaxis, nasal obstruction and a subcutaneous swelling over the left malar region with radiological evidence of a mass in the right nasal cavity. Histology of the lesions showed necrotizing granuloma with evidence of vasculitis. There was no other systemic involvement and the patient was ANCA-negative. Excellent response to systemic steroid and cyclophosphamide therapy was noted.