Meningioangiomatosis: report of three cases and review of the literature
Savargaonkar, P.; Chen, S.; Bhuiya, T.; Valderrama, E.; Bloom, T.; Farmer, P.M.
Annals of Clinical and Laboratory Science 33(1): 115-118
2003
ISSN/ISBN: 0091-7370 PMID: 12661908 Document Number: 563598
Meningioangiomatosis is a rare condition, probably hamartomatous, characterized by proliferation of capillary-sized vessels, meningothelial cells, and fibroblasts within the cortex of the brain. Lesions may be single or diffuse and may be associated with neurofibromatosis type II. Clinically it presents with seizures but may be asymptomatic throughout life. We report 3 cases of meningioangiomatosis, 2 localized and 1 diffuse, all with different clinical manifestations. Differential diagnoses are discussed with a review of the literature. Since this condition is rare, close clinico-pathological correlation is essential. A correct diagnosis avoids further aggressive treatment.