Persistent müllerian duct syndrome
Rizk, D.E.; Ezimokhai, M.; Hussein, A.S.; Gerami, S.; Deb, P.
Archives of Gynecology and Obstetrics 261(2): 105-107
1998
ISSN/ISBN: 0932-0067 PMID: 9544377 DOI: 10.1007/s004040050208Document Number: 533294
We report an 18-month old male presenting with a right-sided inguinal hernia and undescended testes. At herniotomy, a uterus and two fallopian tubes were found in the pelvic peritoneum adjacent to the two gonads which received their blood supply partly along the müllerian duct remnants. The gonads were testes by histological examination. Bilateral orchiopexy was performed without removal of the müllerian structures for fear of jeopardizing the testicular blood supply. The diagnosis of persistent müllerian duct syndrome was confirmed postoperatively by genetic and hormonal investigations.