Sézary syndrome in a Malay--case report and literature review
Yuen, P.; Chan, H.L.; Lee, Y.S.
Singapore Medical Journal 42(5): 224-227
2001
ISSN/ISBN: 0037-5675 PMID: 11513062 Document Number: 531610
Sezary syndrome is a rare form of primary cutaneous T cell lymphoma. It is a distinct systemic variant of mycosis fungoides, marked by erythroderma, lymphadenopathy and circulating cerebriform lymphocytes in the peripheral blood. We report a case of Sezary syndrome in a 61-year-old Malay man with a five-year history of indurated plaques, ulcers and tumours on the head and trunk, with characteristic findings on physical examination, skin biopsy, electron microscopy, immunophenotyping and peripheral blood film. A literature review on Sezary syndrome is presented.