Brachial plexopathy associated with diffuse edematous scleroderma
Mouthon, L.; Halimi, C.; Dussaule Md, J.C.; Cayre-Castel Md, M.; Guillevin, L.
Annales de Medecine Interne 151(4): 303-305
2000
ISSN/ISBN: 0003-410X PMID: 10922959 Document Number: 520572
Peripheral nervous system (PNS) involvement is rare in systemic sclerosis (SSc), usually restricted to peripheral nerve entrapment. To our knowledge, only one case of scleroderma with brachial plexus involvement has been reported previously. We report here on a 61-year-old woman with past history of limited cutaneous SSc who developed motor deficiency in the left arm concomittent with diffuse edematous scleroderma without evidence for trauma or compression of the brachial plexus. After six months intravenous pulse cyclophosphamide therapy, dramatic improvement of skin and neurological involvement was observed.